Center for Consumer Health Information, Cleveland Clinic

 

Pediatric Diseases: Healing Little Hearts

Introduction
Although the prospect of a heart defect in a child is frightening, most children with abnormalities of the heart lead normal or near normal lives, can safely undergo corrective procedures, and have an excellent outlook for long-term survival and quality of life.

What types of heart problems affect children?
Most heart problems in children are congenital, which means they are present or existing at birth. Congenital heart diseases are abnormalities or defects of the heart and its major blood vessels. These heart defects occur in 1 percent of the population and range in severity from simple defects — for example, a ventricular or atrial septal defect (a small hole in the wall between two chambers of the heart) — to complex abnormalities — for example hypoplastic left heart syndrome (an underdeveloped left atrium and ventricle, narrowed valves connecting these chambers, and an abnormally formed aorta).

What is a heart murmur?
Most children have heart murmurs at some time in their lives. A heart murmur is a sound that the doctor can hear with a stethoscope. Normal sounds of vibration or flow within the heart can be heard during routine examination, and these normal sounds are called "innocent" heart murmurs. Innocent murmurs are normal and harmless, and might disappear and reappear from one examination to the next. In most cases, the family doctor or pediatrician can determine which sounds are innocent murmurs and which require further evaluation.

Some murmurs can indicate a heart defect. A pediatric cardiologist can evaluate an unusual or suspicious murmur and determine if further testing is needed. If your child has an innocent murmur, he or she does not have to limit his or her activity, take antibiotics before dental work, or follow any other special precautions.

How are pediatric heart diseases treated?
The treatment and outlook for each child depends on the disease and its severity. In some cases, no treatment is necessary and life expectancy is normal. Many forms of congenital heart defects require some type of treatment at some point in life. The treatment needed might be surgery or treatment using a catheter, a tube passed into an artery and up to the heart. In most cases, treatment for congenital heart disease results in normal or near normal heart function.

In rare cases, the cardiac defect is so severe that normal heart function cannot be established, but surgery is performed to reduce symptoms, improve survival, and allow a normal or near normal quality of life for the child. Surgery for most congenital heart defects currently carries a low risk of death or serious complications (less than 2 percent), and requires a short hospitalization with a rapid return to normal activities.

Although surgery seldom makes the heart completely "normal," most children are able to pursue normal activities, and experience excellent growth and development. Similarly, young adults who have undergone surgical correction of congenital heart defects during childhood generally enjoy good health, pursue normal activities, and maintain an excellent quality of life.

Almost every individual born with a heart defect requires lifetime follow-up and routine cardiac evaluations. An increasing number of adults have survived childhood despite a congenital heart defect, and such individuals benefit from evaluation in a center specialized in adult congenital heart disease. Important issues for young adults include pregnancy, employability, insurability, and activity and exercise prescriptions.

Can heart disease in children cause sudden death?
Sudden death as a result of a heart disease very rarely occurs in children and adolescents. Injury and trauma are much more likely than heart problems to cause death during childhood. Sudden infant death syndrome is only rarely associated with any heart defect or abnormality.

Sudden death during exercise in adolescent athletes is a rare occurrence. Potential cardiac causes of sudden death in this population include:

  1. Hypertrophic cardiomyopathy (enlarged heart muscle)
  2. Myocarditis (inflammation of the heart muscle due to infection)
  3. Marfan's syndrome (an inherited muscle and bone disorder that, in the heart, can cause breaking of the elastic fibers in the walls of the aorta.)
  4. Coronary artery abnormalities
  5. Long QT syndrome (an abnormal heart rhythm)

Careful history and physical examination can identify risk factors for sudden death in most young athletes.

Do children develop hardening of the arteries?
The medical term for hardening of the arteries is "atherosclerosis." Atherosclerosis is the buildup of plaque (hard deposits) in the artery walls. This buildup can block the artery and promote the formation of blood clots.

Atherosclerosis of the arteries around the heart is a type of coronary artery disease. Children generally do not develop problems from coronary artery disease. However, mild abnormal changes can be seen in the walls of arteries of children, and damage to the arteries can begin during childhood.

Risk factors for the development of atherosclerosis include:

  • A family history of atherosclerosis
  • A sedentary lifestyle
  • Obesity
  • Smoking
  • Abnormal serum lipids (high levels of fat, including cholesterol, in the blood)

Nearly all of these factors can be modified during childhood. Avoidance of cigarette smoking and increased aerobic exercise — along with weight control and blood pressure monitoring — should be encouraged to promote a healthy cardiovascular lifestyle and to reduce cardiovascular risk factors in children, adolescents, and young adults.

In rare cases, a lipid disorder, such as familial hypercholesterolemia, might be present. This disorder causes excess amounts of cholesterol in the blood and requires following a special diet and taking medicines.

Summary

  1. Most children with heart disease are born with a congenital heart defect. The life expectancy and quality of life for most of these children are excellent.
  2. Most heart murmurs in children are innocent and require no treatment.
  3. The risk of sudden cardiac death in children and adolescents is very low. Many cardiac causes can be identified by taking a careful history and performing a physical examination.
  4. The risk factors for the development of atherosclerosis are present in childhood. Adoption of healthy lifestyles during childhood should reduce the impact of atherosclerosis in adults.

© Copyright 1995-2008 The Cleveland Clinic Foundation. All rights reserved

This information is provided by the Cleveland Clinic and is not intended to replace the medical advice of your doctor or health care provider. Please consult your health care provider for advice about a specific medical condition. For additional written health information, please contact the Health Information Center at the Cleveland Clinic (216) 444-3771 or toll-free (800) 223-2273 extension 43771 or visit www.clevelandclinic.org/health/.

index#5569